2-Hydroxy-2-methylbutanoicacid是一种非正常的代谢物，和羟基戊二酸尿症以及枫糖尿病有关。
CAS：3739-30-8
分子式：C5H10O3
分子量：118.13
纯度：98%
存储：Store at -20°C

Background:

2-Hydroxy-2-methylbutanoic acid, an unusual metabolite, is associated with 2-hydroxyglutaric aciduria and maple syrup urine disease.

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