H-HoPro-OH是赖氨酸的分解产物，它能在患有常染色体遗传性疾病的婴儿体液中积累，比如Zellweger综合征，新生儿肾上腺机能障碍。
CAS：3105-95-1
分子式：C6H11NO2
分子量：129.16
纯度：98%
存储：Store at -20°C

Background:

H-HoPro-OH is a breakdown product of lysine, accumulates in body fluids of infants with generalized genetic peroxisomal disorders, such as Zellweger syndrome, neonatal adrenoleukodystrophy.

[1]. Mihalik SJ, et al. Peroxisomal L-pipecolic acid oxidation is deficient in liver from Zellweger syndrome patients. Pediatr Res. 1989 May;25(5):548-52.