规格: | 98% |
分子量: | 295.2 |
包装 | 价格(元) |
25mg | 电议 |
100mg | 电议 |
500mg | 电议 |
Background:
DL-Cystathionine is an intermediate in the synthesis of cysteine that is produced from homocysteine and serine by the action of cystathionine-β-synthase (CBS). CBS can also mediate the condensation of cysteine with homocysteine to produce cystathionine and hydrogen sulfide. An excess of cystathionine in the urine, resulting from a congenital deficiency of cystathionase or an acquired deficiency of vitamin B6, is a hallmark of cystathioninuria.